Anesthetic management of emergency cesarean section in a woman with lipoid proteinosis

  • Korich Noureddine
  • Khalil Shibli
  • Ibrahim EL Boursaly
  • Sanjeev D Jain Specialist Anesthesiologist Department of Anesthesiology, ICU and Perioperative Medicine, Hamad Medical Corporation, Doha (Qatar)
  • Zahir Lemtai
Keywords: Lipoid proteinosis, Anesthesia, Lipoid proteinosis General, Anesthesia Regional, Difficult airway, Endotracheal intubation

Abstract

Lipoid proteinosis is a rare autosomal recessive disorder of generalized thickening of the skin, mucosa, and certain viscera due to deposition of numerous small clumps of proteins that give the skin a yellowish color. Lipoid deposits in upper respiratory tract, mucous membranes of the mouth and in vocal cords may interfere with airway management during general anesthesia, and hence the regional techniques are usually preferred in known cases. Here the authors present a typical known case of lipoid proteinosis, which presented for emergency cesarean section due to abruptio placentae. She was meticulously managed with spinal anesthesia.
Citation: Noureddine K, Shibli K, EL Boursaly  I, Jain SD, Lemtai Z. Anesthetic management of emergency cesarean section in a woman with lipoid proteinosis. Anaesth Pain & Intensive Care 2018;22(4):­­515-517
Received – 4 Nov 2018; Reviewed – 5 Dec 2018; Corrected & Accepted – 31 Dec 2018

Published
07-09-2019
How to Cite
Noureddine, K., Shibli, K., EL Boursaly, I., Jain, S. D., & Lemtai, Z. (2019). Anesthetic management of emergency cesarean section in a woman with lipoid proteinosis. Anaesthesia, Pain & Intensive Care, 22(4). Retrieved from https://mail.apicareonline.com/index.php/APIC/article/view/1039
Section
Case Reports